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KMID : 0387820140210010029
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Clinical Pediatric Hematology-Oncology
2014 Volume.21 No. 1 p.29 ~ p.32
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A Case of Glanzmann’s Thrombasthenia Successfully Managed after Tonsillectomy
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Choi Jeong-Seok
Jung Gi-Hwa
Lim Jae-Yol
Kim Young-Mo
Kim Soon-Ki
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Abstract
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Glanzmann’s thrombasthenia (GT) is a rare autosomal recessive disease and platelet function disorder, in which platelet membrane GP IIb/ IIIa complex is defective and platelet aggregation is undeveloped. GT is characterized by mucocutaneous hemor-rhages, such as, epistaxis, purpura, gingival bleeding, and menorrhagia, severe bleeding complications during surgery. We report the case of a 6-year-old boy with GT who un-derwent tonsillectomy. Here, we focus on perioperative hemostatic management using recombinant factor VIIa, fibrin glue and hemostat materials.
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KEYWORD
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Glanzmann’s thrombasthenia, Tonsillectomy, Hemostasis
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